상악골에 발생한 침습성 섬유종증의 치험례
AGGRESSIVE FIBROMATOSIS OF THE MAXILLA
소속 상세정보
최재선/Jae-Sun Choi
이계혁/김호성/성대경/김건중/정종철/하승연/조현이/Gye-Hyeok Lee/Ho-Sung Kim/Dae-Kyung Sung/Keon-Jung Kim/Jong-Cheol Jeong/Seung-Yeon Ha/Hyun-I Cho
KMID : 0355619980240020241
Abstract
저자 등은 10세 여자 환자의 상악 우측 치조골에 침습성 섬유종증을 치험하였으며 이는
임상검사상 섬유육종과 매우 유사하므로 정확한 임상소견과 조직검사에 의한 주의깊은 진단
이 요구되리라 사료된다.
#초록#
Aggressive fibromatosis is best difined as a group of non-encapsulated,
non-metastasizing fibrous tumors that have tendency for local recurrence. This tumor is
chariaterized histologically by fibroblastic proliferation and clinically by the potential to
infiltrate and to recur after surgical excision, but not metastasize. The most common
anatomic location have been the abdominal muscle and the extrimities. The incidence of
the head and neck is mentioned as from 9.5% to 50% of all desmoid tumors. Within this
area, 40%-to 80% of the tumors are located in the neck, but rare in oral cavity.
Histologically the tumor is composed of proliferative fibroblasts with a collagenous
component. The degree of cellularity varies from area to area and from tumor to tumor.
The cells are usually spindle-shaped and the nuclei present only slightly polymorphism,
but mitosis are rare and never atypical.
Oral fibromatosis has been described as fibrosarcoma, pseusarcoma, pseudosarcomatous
fibrosarcoma, metastasizing fibromatosis, juvenile aggressive fibromatosis, and aggressive
fibromatosis, but Wilkin and Waldron suggested that the aggressive fibromatosis was a
more appropriate term, reflecting the invasive characteristics of the tumor.
The treatment of aggressive fibromatosis is traditionally surgical resection with an
area of tumor free tissue. But when the complete surgical excision is not possible,
radiation and chemotherapy also can be used.
Clinically the tumor reported to be not painful in most cases, but capable of rapid
growth. Careful clinical and histological examinations are essential for correct diagnosis.
We report a case of aggressive fibromatosis. Occurring of the maxilla in 10 year female
patient.
키워드
Aggressive fibromatosis; Complete surgical excision;
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